METAX
XPhe Smart J
Highly concentrated, low-volume amino acid mixture for school-age children with PKU
Medical Condition
Phenylketonuria (PKU), hyperphenylalaninaemia (HPA)
Age Group
School-age children (7–14 years)
Dosage Form
Powder for reconstitution as a gel, drink or shake
Packaging
14.5 g sachet or 500 g tin
Storage Conditions
Composition (key components)
Highly purified phenylalanine-free L-amino acids; a small amount of carbohydrates (no fat); vitamins, minerals and trace elements
XPhe Smart J is a Food for Special Medical Purposes (FSMP) designed for children with phenylketonuria (PKU) or hyperphenylalaninaemia (HPA) aged 7 to 14 years. The formula contains highly purified L-amino acids free from phenylalanine and combines a high protein equivalent concentration with a small intake volume.
Key features
Phenylalanine-free
For children aged 7–14 years
Highly concentrated, low-volume amino acid mixture
10 g protein equivalent (PE) per sachet, or 70 g PE per 100 g of dry powder
Low-calorie formula
Contains a small amount of carbohydrates and no fat
Highly purified L-amino acids
Flexible preparation options: gel, drink and shake
Fortified with vitamins, minerals and trace elements
4 flavour options: neutral, lemon, forest berries, vanilla
Format: 14.5 g sachet or 500 g tin
XPhe Smart J follows the concept of low-volume metabolic therapy — the product can be prepared at different concentrations, from a thick gel to a ready-to-drink shake. This allows the amino acid mixture to be adapted to the child's daily routine, school schedule and individual taste preferences.
flexible low-volume concept for active school-age children
XPhe Smart J is designed for those who need to:
reduce the intake volume of the amino acid mixture
improve adherence to dietary therapy
make it easier to take the mixture at school or during an active day
adapt the product's consistency to their own preferences
The product's low energy value allows for more flexible planning of the individual energy intake according to the patient's clinical needs.
Flexible low-volume concept
XPhe Smart J can be prepared in different textures and volumes depending on the patient's needs:
Clinical role in PKU management
XPhe Smart J replaces the portion of dietary protein that cannot be obtained from natural food sources due to impaired phenylalanine metabolism. The daily amount of the amino acid mixture is determined individually based on age, body weight, phenylalanine tolerance, and the results of regular metabolic monitoring.
The daily dose should be divided into 3–5 separate servings throughout the day. XPhe Smart J can be combined with other products in the XPhe range according to the patient's individual dietary plan.
Practical use
XPhe Smart J should be prepared immediately before consumption. After taking the concentrated XS, S or M forms, it is recommended to additionally drink a glass of water or another beverage.
